Sjogren's Syndrome ICD-10-CM Codes | 2023

Navigate Sjogren's Syndrome coding with our comprehensive guide on ICD-10 codes, ensuring accurate diagnosis and billing for 2023.

By Ericka Pingol on Feb 29, 2024.

Fact Checked by Ericka Pingol.

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Sjogren's Syndrome ICD-10-CM Codes | 2023

What ICD-10 Codes are Used for Sjogren's Syndrome?

Sjogren's Syndrome, an autoimmune disorder primarily affecting the exocrine glands, is categorized under several ICD-10 codes depending on the organs involved. Below is a refined list of these codes with enhanced clinical descriptions:

  • M35.00 - Sjogren's syndrome, unspecified: This code is applied when a patient is diagnosed with Sjogren's Syndrome but the specific organ involvement is not detailed in the documentation.
  • M35.01 - Sjogren's syndrome with keratoconjunctivitis: Indicates Sjogren's Syndrome with ocular involvement, characterized by dryness of the eyes (keratoconjunctivitis sicca) due to lymphocytic infiltration of lacrimal glands.
  • M35.02 - Sjogren's syndrome with lung involvement: Used when Sjogren's Syndrome manifests with pulmonary complications, which may include interstitial lung disease or other pulmonary function impairments.
  • M35.03 - Sjogren's syndrome with myopathy: Assigned to cases where Sjogren's Syndrome presents with muscle involvement, leading to symptoms such as muscle weakness and pain.
  • M35.04 - Sjogren's syndrome with nervous system involvement: Applicable for neurological complications associated with Sjogren's Syndrome, which can range from peripheral neuropathy to central nervous system manifestations.
  • M35.09 - Sjogren's syndrome with other organ involvement: This code is reserved for instances where Sjogren's Syndrome affects organs other than those specified in codes M35.01 to M35.04, such as the kidneys, liver, or pancreas.

For a visual and comprehensive explanation of how to apply these ICD-10 codes in clinical documentation, please view our explainer video on Sjogren's Syndrome ICD Codes.

Which Sjogren's Syndrome ICD codes are Billable?

  • M35.00 - Yes
  • M35.01 - Yes
  • M35.02 - Yes
  • M35.03 - Yes
  • M35.04 - Yes
  • M35.09 - Yes

Clinical Information

  • Sjogren's Syndrome is a systemic autoimmune condition with hallmark symptoms and various systemic manifestations.
  • Persistent dry eyes (keratoconjunctivitis sicca) and dry mouth (xerostomia) due to the destruction of salivary and lacrimal glands by autoimmune processes.
  • Dryness can lead to complications such as dental caries, oral candidiasis, and corneal ulceration.
  • May present with extra glandular involvement such as arthralgia, arthritis, and myalgia, contributing to joint pain and swelling.
  • Fatigue and myalgia are common, significantly impacting the quality of life.
  • Blood tests reveal specific autoantibodies (e.g., Anti-SSA/Ro and Anti-SSB/La). Schirmer's test and other ocular tests are used to assess tear production.
  • Salivary gland biopsy may be performed to detect lymphocytic infiltration indicative of the syndrome.
  • Symptomatic treatment includes artificial tears, saliva substitutes, and saliva stimulants to alleviate dryness.
  • Systemic immunosuppressive therapy may be indicated for patients with severe extra glandular manifestations.
  • Regular dental check-ups and oral hygiene are crucial due to the increased risk of dental problems.
  • Regular monitoring for the development of systemic complications such as interstitial lung disease, renal tubular acidosis, and lymphoma.
  • Follow-up with rheumatology for systemic disease management and with ophthalmology for ocular care.

Synonyms Include:

  • Sicca syndrome
  • Autoimmune exocrinopathy
  • Glandular disease, Sjogren's
  • Lymphocytic sialadenitis
  • Keratoconjunctivitis sicca
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Commonly asked questions

When to use a Sjogren's Syndrome ICD code?

Use when a patient is diagnosed with Sjogren's Syndrome, confirmed by clinical evaluation and diagnostic tests.

What are the common treatments for Sjogren's Syndrome Diagnosis Codes?

Treatments include symptomatic relief measures, immune system suppressants, and addressing specific organ involvement.

What does a diagnosis code for Sjogren's Syndrome mean?

It indicates a medical diagnosis of Sjogren's Syndrome, which is essential for treatment plans and insurance billing.

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