What ICD-10 Codes are Used for Sjogren's Syndrome?
Sjogren's Syndrome, an autoimmune disorder primarily affecting the exocrine glands, is categorized under several ICD-10 codes depending on the organs involved. Below is a refined list of these codes with enhanced clinical descriptions:
- M35.00 - Sjogren's syndrome, unspecified: This code is applied when a patient is diagnosed with Sjogren's Syndrome but the specific organ involvement is not detailed in the documentation.
- M35.01 - Sjogren's syndrome with keratoconjunctivitis: Indicates Sjogren's Syndrome with ocular involvement, characterized by dryness of the eyes (keratoconjunctivitis sicca) due to lymphocytic infiltration of lacrimal glands.
- M35.02 - Sjogren's syndrome with lung involvement: Used when Sjogren's Syndrome manifests with pulmonary complications, which may include interstitial lung disease or other pulmonary function impairments.
- M35.03 - Sjogren's syndrome with myopathy: Assigned to cases where Sjogren's Syndrome presents with muscle involvement, leading to symptoms such as muscle weakness and pain.
- M35.04 - Sjogren's syndrome with nervous system involvement: Applicable for neurological complications associated with Sjogren's Syndrome, which can range from peripheral neuropathy to central nervous system manifestations.
- M35.09 - Sjogren's syndrome with other organ involvement: This code is reserved for instances where Sjogren's Syndrome affects organs other than those specified in codes M35.01 to M35.04, such as the kidneys, liver, or pancreas.
For a visual and comprehensive explanation of how to apply these ICD-10 codes in clinical documentation, please view our explainer video on Sjogren's Syndrome ICD Codes.

