ILD ICD-10-CM Codes

ILD ICD-10-CM Codes

Discover essential ICD-10 codes used for Interstitial Lung Disease (ILD). Proper coding for accurate diagnosis and billing. Learn more about ILD ICD codes.

By Katherine Ellison on Aug 8, 2025.

Fact Checked by Ericka Pingol.

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What ICD-10 Codes are Used for ILD? 

Interstitial Lung Disease (ILD) is a complex medical condition that can cause significant damage to the lungs. It encompasses a group of lung disorders characterized by inflammation and scarring of the lung tissue, which can impair its ability to expand and contract efficiently. This, in turn, can lead to a range of symptoms, including shortness of breath, coughing, and fatigue.

When diagnosing and treating ILD, healthcare professionals often rely on a system of diagnostic codes known as ICD-10. These codes help identify the specific type of ILD a patient may be experiencing and provide clinicians with a clinical description of the condition.

Here are 6 commonly used ICD-10 codes for various types of ILD, along with their clinical descriptions:

  1. J84.112 - Idiopathic Pulmonary Fibrosis (IPF): IPF, a lung disease with unknown origin, is characterized by the scarring and fibrosis of lung tissue, which results in reduced lung function and shortness of breath.
  2. J84.89 - Other Interstitial Pulmonary Diseases: This particular code encompasses a variety of ILDs that do not fall into any specific categories, such as ILDs associated with respiratory bronchiolitis and non-specific interstitial pneumonia.
  3. J84.9 - Interstitial Pulmonary Disease, Unspecified: When lung tissue experiences inflammation and scarring, it may indicate an ILD that has not been diagnosed or documented with a specific type.
  4. J84.848 - Lymphangioleiomyomatosis (LAM): LAM is a condition characterized by the uncontrolled growth of unusual smooth muscle-like cells in the lungs, leading to cysts and airway constriction.
  5. J84.170 - Cryptogenic Organizing Pneumonia (COP): COP is a respiratory condition that causes inflammation and the growth of granulation tissue in the bronchioles and alveoli. This leads to coughing, fever, and shortness of breath.
  6. J84.10 - Alveolar and Paracardial Pneumopathy: Various pulmonary diseases, such as desquamative interstitial pneumonia and pulmonary alveolar proteinosis, involve accumulating cellular debris or proteinaceous material in the alveoli.

Please note that the provided ICD-10 codes and clinical descriptions are for educational purposes and should be used in consultation with medical professionals for accurate coding. For more in-depth information on ILD ICD codes and medical billing, you can watch this video: 

Which ILD ICD codes are Billable: 

Here's the list of commonly used ILD ICD-10 codes, along with their billable status:

  1. J84.112 - Idiopathic Pulmonary Fibrosis (IPF): Yes
  2. J84.89 - Other Interstitial Pulmonary Diseases: Yes
  3. J84.9 - Interstitial Pulmonary Disease, Unspecified: Yes
  4. J84.848 - Lymphangioleiomyomatosis (LAM): Yes
  5. J84.170 - Cryptogenic Organizing Pneumonia (COP): Yes
  6. J84.10 - Alveolar and Paracardial Pneumopathy: Yes

Please note that the billable status of ICD-10 codes can depend on various factors, including medical necessity, documentation, and specific coding guidelines. It's recommended to consult with medical billing professionals and relevant coding resources for accurate and up-to-date billing information.

Clinical Information

  • ILD refers to a group of lung disorders characterized by inflammation and scarring of the interstitium, the tissue between the air sacs in the lungs. This scarring can lead to reduced lung function and impaired gas exchange.
  • Common symptoms include shortness of breath, persistent cough, fatigue, chest discomfort, and, in advanced cases, respiratory failure. Symptoms can vary based on the specific type of ILD.
  • ILD encompasses various types, including idiopathic pulmonary fibrosis (IPF), sarcoidosis, connective tissue disease-associated ILD, hypersensitivity pneumonitis, and more. Each type has distinct clinical and pathological features.
  • The causes of ILD are diverse and may include exposure to environmental toxins (asbestos, silica), autoimmune conditions (rheumatoid arthritis, systemic sclerosis), infections, medication side effects, and genetic predisposition.
  • Diagnosis involves clinical assessment, imaging (high-resolution CT scans), pulmonary function tests, and sometimes lung biopsy. Differentiating between ILD types is crucial for appropriate management.
  • Treatment aims to alleviate symptoms, slow disease progression, and improve quality of life. Management approaches include medications (corticosteroids, immunosuppressants), oxygen therapy, pulmonary rehabilitation, and, in some cases, lung transplantation.
  • The prognosis for ILD varies widely depending on the specific type, the extent of scarring, and the individual's overall health. Some ILDs have a gradual progression, while others may worsen rapidly.
  • ILD often requires a collaborative approach involving pulmonologists, rheumatologists (for autoimmune-associated ILD), radiologists, pathologists, and sometimes thoracic surgeons for biopsies or transplant evaluation.
  • Ongoing research aims to understand the underlying mechanisms of ILD better and develop more targeted therapies. Advances in imaging techniques and molecular biology contribute to earlier and more accurate diagnoses.
  • ILD patients benefit from education about their condition, lifestyle adjustments, and support groups to cope with the challenges of living with a chronic lung disease.

Synonyms Include

  • Diffuse Parenchymal Lung Disease
  • Diffuse Lung Disease
  • Interstitial Pneumonia
  • Pulmonary Fibrosis
  • Restrictive Lung Disease
  • Diffuse Interstitial Lung Disease
  • Interstitial Lung Disorders
  • Lung Fibrosis
  • Pulmonary Interstitial Fibrosis
  • Interstitial Pulmonary Fibrosis
Medical Billing and Coding Software

Commonly asked questions

Use an ILD ICD code when diagnosing a patient with any type of Interstitial Lung Disease to accurately document their condition for medical records and billing purposes.

Yes, ILD diagnoses are billable when submitting healthcare claims. Properly coded diagnoses are crucial for accurate billing and insurance reimbursement.

Common treatments include medications (corticosteroids, immunosuppressants), oxygen therapy, pulmonary rehabilitation, and, in severe cases, lung transplantation.

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