What ICD-10 codes are used for pulmonary hypertension?
Pulmonary hypertension is a form of high blood pressure that affects the pulmonary arteries, impairing blood flow between the heart and lungs. It can be primary pulmonary hypertension (idiopathic/heritable) or secondary pulmonary hypertension caused by another condition, including lung disease, congenital heart disease, liver disease, chronic kidney disease, or sleep apnea.
The following ICD-10-CM codes are used to document and bill for pulmonary hypertension:
- I27.0 – Primary pulmonary hypertension
- I27.2 – Other secondary pulmonary hypertension (category only)
- I27.20 – Pulmonary hypertension, unspecified; used when the exact type of pulmonary hypertension unspecified is not diagnosed.
- I27.21 – Secondary pulmonary arterial hypertension; typically linked to conditions such as connective tissue disease, congenital heart disease, or HIV.
- I27.22 – Pulmonary hypertension due to left heart disease; common in patients with hypertensive disease, heart failure, or valvular disease.
- I27.23 – Pulmonary hypertension due to lung diseases and/or hypoxia; applies to interstitial lung disease, COPD, or obstructive sleep apnea
- I27.24 – Chronic thromboembolic pulmonary hypertension (CTEPH); related to a history of pulmonary embolism or chronic clot burden in pulmonary vessels.
- I27.29 – Other specified secondary pulmonary hypertension; includes cases from hematologic disorders, metabolic disorders, toxin-induced pulmonary hypertension, and unclear multifactorial mechanisms such as systemic disorders code conditions or chronic myeloid leukemia.