Myasthenia Gravis ICD-10-CM Codes

Check our short guide to the ICD-10 codes used for myasthenia gravis to know more about the codes' clinical description, billability, synonyms, and more.

By Ericka Pingol on Aug 8, 2025.

Fact Checked by Karina Jimenea.

Use Code

What ICD-10 codes are used for myasthenia gravis?

Myasthenia gravis is a chronic autoimmune and neuromuscular disorder that disrupts nerve and muscle communication, causing weakness in the skeletal muscles. For billing and coding purposes, here are the most commonly used ICD-10 codes:

G70.00: Myasthenia gravis without (acute) exacerbation: Used when the patient’s condition is stable and symptoms are not currently worsening.
G70.01: Myasthenia gravis with (acute) exacerbation: Used when the patient is experiencing a significant flare-up or worsening of symptoms, such as respiratory or swallowing difficulties.
P94.0: Transient neonatal myasthenia gravis: Used for newborns temporarily affected by maternal antibody transfer; symptoms are usually self-limited.
G70.2: Congenital and developmental myasthenia – Used when the condition is present from birth and not acquired later in life.
G70.80: Lambert-Eaton syndrome, unspecified: Used for an autoimmune myoneural disorder often associated with malignancy or small-cell lung cancer.
G70.81: Lambert-Eaton syndrome in disease classified elsewhere: Used for an autoimmune myoneural disorder often associated with malignancy or small-cell lung cancer.
G70.89: Other specified myoneural disorders: Used when a diagnosed myoneural disorder does not fit into any of the other specified categories.
G70.9: Myoneural disorder, unspecified – Used when symptoms suggest a myoneural disorder, but a specific diagnosis has not been confirmed.

Which myasthenia gravis ICD codes are billable?

All myasthenia gravis codes are billable.

Clinical information

Myasthenia gravis is a chronic autoimmune and neuromuscular disorder in which the body produces antibodies that interfere with the communication between nerves and muscles. This disruption impairs the function of skeletal muscles, leading to muscle weakness that worsens with activity and improves with rest.
Common symptoms include ptosis (drooping eyelids), diplopia (double vision), facial paralysis, slurred speech, difficulty chewing or swallowing, shortness of breath, and generalized muscle fatigue. In severe cases, the weakness can affect respiratory muscles, leading to a myasthenic crisis, a potentially life-threatening condition requiring urgent intervention.
The cause is not fully understood but may involve abnormalities in the thymus gland or the presence of acetylcholine receptor (AChR) antibodies or MuSK antibodies. Some cases are associated with thymoma. The disorder may occur at any age but is more common in women under 40 and men over 60.
Transient neonatal myasthenia gravis may occur in newborns due to the passive transfer of maternal antibodies. This condition is typically temporary and resolves as the antibodies are cleared from the infant’s circulation.
Diagnosis involves a combination of clinical evaluation, neurological examination, antibody testing, electrophysiological studies (such as repetitive nerve stimulation or single-fibre EMG), and imaging studies to assess the thymus.
Treatment options include acetylcholinesterase inhibitors, corticosteroids, immunosuppressants, intravenous immunoglobulin (IVIG), plasmapheresis, and thymectomy in selected cases. Lifestyle adjustments and supportive therapies are also recommended to manage fatigue and maintain function.

Synonyms include

Myasthenic crisis
Generalized myasthenia
Myasthenia gravis, adult form
Ocular myasthenia
Rippling muscle disease with myasthenia gravis
Toxic myoneural disorders

Commonly asked questions

A myasthenia gravis ICD code is used when a patient presents with signs of impaired communication at the myoneural junction and muscle, such as fluctuating muscle weakness or fatigue, and is diagnosed with myasthenic syndromes based on clinical and neurological assessments. It falls under nervous system disorders, specifically gravis and other myoneural disorders.

Yes, myasthenia gravis diagnoses are billable, which allows for reimbursement when properly documented and supported by medical evidence.

Treatments include acetylcholinesterase inhibitors, immunosuppressive therapy, plasmapheresis, IVIG, and thymectomy—all targeting symptoms related to the myoneural junction and muscle. Supportive care and monitoring are essential for preventing complications like myopathy not elsewhere classified.

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